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Abstract #25319 Published in IGR 12-1
High measured intraocular pressure in children with recessive congenital hereditary endothelial dystrophy
Khan A O; Al-Shehah A; Ghadhfan F EJournal of Pediatric Ophthalmology & Strabismus 2010; 47: 29-33
Purpose: To report the phenomenon of high measured intraocular pressure in recessive congenital hereditary endothelial dystrophy. Methods: A case series was retrospectively reviewed. Results: Five infants with significant congenital corneal haze had increased measured intraocular pressure that remained high despite drug treatment and surgery to decrease intraocular pressure. The clinical diagnosis of recessive congenital hereditary endothelial dystrophy without glaucoma was made based on the absence of buphthalmos, a distinct pattern of mosaic corneal haze with significant corneal thickness, and absence of cupping in healthy-appearing optic nerve heads. Conclusion: Intraocular pressure can be falsely elevated in some children with recessive congenital hereditary endothelial dystrophy, leading to confusion with congenital glaucoma.
A. O. Khan. King Khaled Eye Specialist Hospital, P. O. Box 7191, Riyadh 11462, Saudi Arabia.
Classification:
9.4.2.3 Fuchs' endothelial dystrophy (Part of: 9 Clinical forms of glaucomas > 9.4 Glaucomas associated with other ocular and systemic disorders > 9.4.2 Glaucomas associated with disorders of the cornea, conjunctiva, sclera)
9.1.1 Congenital glaucoma, Buphthalmos (Part of: 9 Clinical forms of glaucomas > 9.1 Developmental glaucomas)
