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Abstract #5313 Published in IGR 1-2
A case of congenital glaucoma with hydrocephalus due to myelomeningocele
Nemoto D; Fukuchi T; Hara H; Ohta A; Suda K; Funaki S; Shirakashi M; Abe H; Sawaguchi SFolia Ophthalmologica Japonica / Nihon Ganka Kiyo 1999; 50: 146-149
We report on a 4-month-old boy with congenital glaucoma and hydrocephalus due to myelomeningocele. The patient was born by cesarean section at a gestational age of 32 weeks and 3 days. A myelomeningocele that had been identified in the patient's sacral region by ultrasonic examination was closed by surgery performed on the day of birth. Four months after birth, the patient was found to have increased intraocular pressure (30 mmHg in the right eye and 25 mmHg in the left eye) and trabeculotomy was performed on both eyes. After trabeculotomy, intraocular pressure remained in the normal range without any medications. However, the patient's right iris was white- gray with the sphincter muscle visible. The anterior chamber angle showed wrap-around type high-insertion in both eyes, a vascular ring and micro capillaries in the right eye. The association of hydrocephalus and congenital glaucoma may occur in Walker Warburg syndrome and in syndromes and diseases with chromosomal anomalies or phacomatosis such as Sturge-Weber syndrome or Von Recklinghausen disease. As long as we continued follow-up examinations in this case, it did not meet criteria for any of these syndromes or diseases.LA: Japanese
Dr. D. Nemoto, Dept of Ophthalmol, Niigata Univ School of Med, 1-757, Asahimachidori, Niigata 951-8510; Japan
Classification:
9.1.1 Congenital glaucoma, Buphthalmos (Part of: 9 Clinical forms of glaucomas > 9.1 Developmental glaucomas)
