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Abstract #59471 Published in IGR 16-3
Adult Sturge-Weber syndrome without facial hemangioma: report of one case
Zhang R; Chen W; Hu Q; Shrestha SZhejiang Da Xue Xue Bao Yi Xue Ban 2014; 43: 588-590
Sturge-Weber syndrome (SWS) is characterized by angiomas affecting the ophthalmic division of the trigeminal nerve, epilepsy, intellectual impairment, hemiplegia and glaucoma. We report a patient who developed SWS without facial hemangioma (SWS type Ⅲ) in his adulthood. The patient presented with repeated episodes of headache since age 37 year. He manifested first attack of seizure at the age 47 year followed by aphasia and right upper limb palsy. Brain CT scan revealed right parietal-occipital calcification, brain CT angiography showed right temporal lobe and occipital lobe vascular malformation, and MRI showed leptomeningeal enhancement in the riht cerebral piamater. The seizure was controlled with antiepileptic drugs and reviewed in routine follow up.
Department of Ophthalmology, Shaoxing Peoples Hospital, Shaoxing 312000, China;College of Optometry, Wenzhou Medical University, Wenzhou 325027, China.
Classification:
9.4.15 Glaucoma in relation to systemic disease (Part of: 9 Clinical forms of glaucomas > 9.4 Glaucomas associated with other ocular and systemic disorders)
